Research map: The Spectrum of Pulmonary Perivascular Epithelioid Cell Tumors (PEComa)

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Papers in this map

  1. Efficacy and Safety of Sirolimus in Lymphangioleiomyomatosis · Francis X. McCormack · 2011 · 1129 citations · Cited by this paper
  2. DICER1 Syndrome and Tumor Pathology: An Updated Review for Diagnostic Practice · 2026 · Related
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  5. Thoracic Lymphangiomas, Lymphangiectasis, Lymphangiomatosis, and Lymphatic Dysplasia Syndrome · John L. Faul · 2000 · 420 citations · Cited by this paper
  6. TFE-Altered Renal Cell Carcinoma: A Contemporary Review With Practical Insights and Diagnostic Pearls for Surgical Pathologists · 2026 · Related
  7. Official American Thoracic Society/Japanese Respiratory Society Clinical Practice Guidelines: Lymphangioleiomyomatosis Diagnosis and Management · Francis X. McCormack · 2016 · 374 citations · Cited by this paper
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  9. Lymphangioleiomyomatosis Diagnosis and Management: High-Resolution Chest Computed Tomography, Transbronchial Lung Biopsy, and Pleural Disease Management. An Official American Thoracic Society/Japanese Respiratory Society Clinical Practice Guideline · Nishant Kumar Gupta · 2017 · 261 citations · Cited by this paper
  10. Role of Surrogate Immunohistochemistry Markers in CNS Tumors in the Era of Molecular Diagnostics With Recent Updates · 2026 · Related
  11. Glucose Addiction of TSC Null Cells Is Caused by Failed mTORC1-Dependent Balancing of Metabolic Demand with Supply · Andrew Y. Choo · 2010 · 255 citations · Cited by this paper
  12. Somatic Tumor-Like Neoplasms Arising With Testicular Germ Cell Tumors: Distilling Evolving Understanding, Terminology, and Implications for the Practicing Surgical Pathologist · 2026 · Related
  13. Lymphangioleiomyomatosis: pathogenesis, clinical features, diagnosis, and management · Cormac McCarthy · 2021 · 209 citations · Cited by this paper
  14. Intraepithelial Penile Lesions · 2026 · Related
  15. Changes in Lung Function and Chylous Effusions in Patients With Lymphangioleiomyomatosis Treated With Sirolimus · Angelo M. Taveira‐DaSilva · 2011 · 205 citations · Cited by this paper
  16. An Update on Soft Tissue Tumors of the Paratesticular Region · 2026 · Related
  17. Lymphangioleiomyomatosis: Calling It What It Is: A Low-Grade, Destructive, Metastasizing Neoplasm · Francis X. McCormack · 2012 · 205 citations · Cited by this paper
  18. Histopathology of Autoimmune Hepatitis: An Update · 2025 · Related
  19. Immunohistochemical study of matrix metalloproteinases (MMPs) and their tissue inhibitors (TIMPs) in pulmonary lymphangioleiomyomatosis (LAM) · Tomayoshi Hayashi · 1997 · 187 citations · Cited by this paper
  20. Pathobiology and Interactions of the MiTF Signaling Pathways · 2026 · Related
  21. Clear Cell Tumor of the Lung Immunohistochemical and Ultrastructural Evidence of Melanogenesis · Michael James Gaffey · 1991 · 155 citations · Cited by this paper
  22. Lymphangiomyoma, a benign lesion of chyliferous lymphatics synonymous with lymphangiopericytoma · John L. Cornog · 1966 · 148 citations · Cited by this paper
  23. Lymphangioleiomyomatosis (LAM) · Victor J. Ferrans · 2000 · 146 citations · Cited by this paper
  24. Diffuse pulmonary lymphangiomatosis · Henry D. Tazelaar · 1993 · 140 citations · Cited by this paper
  25. Renal Angiomyolipoma With Sarcomatous Transformation and Pulmonary Metastases · Judith A. Ferry · 1991 · 130 citations · Cited by this paper
  26. Micronodular Pneumocyte Hyperplasia · Trudie E. Muir · 1998 · 123 citations · Cited by this paper
  27. Single-Cell Transcriptomic Analysis Identifies a Unique Pulmonary Lymphangioleiomyomatosis Cell · Minzhe Guo · 2020 · 119 citations · Cited by this paper
  28. Clear Cell Tumor of the Lung. A Clinicopathologic, Immunohistochemical, and Ultrastructural Study of Eight Cases · Michael James Gaffey · 1990 · 117 citations · Cited by this paper
  29. Radiological evidence of lymphangioleiomyomatosis in female and male patients with tuberous sclerosis complex · Miraude E. A. P. M. Adriaensen · 2011 · 115 citations · Cited by this paper
  30. Aortic aneurysms in children and young adults with tuberous sclerosis: Report of two cases and review of the literature · Corey J. Jost · 2001 · 113 citations · Cited by this paper
  31. The NHLBI LAM Registry · Nishant Kumar Gupta · 2018 · 110 citations · Cited by this paper
  32. Pulmonary Cysts of Birt-Hogg-Dubé Syndrome · Mitsuko Furuya · 2012 · 103 citations · Cited by this paper
  33. Pulmonary Lymphangioleiomyomatosis in a Karyotypically Normal Man without Tuberous Sclerosis Complex · M Schiavina · 2007 · 91 citations · Cited by this paper
  34. Pulmonary manifestations in tuberous sclerosis complex · Nishant Kumar Gupta · 2018 · 85 citations · Cited by this paper
  35. Lymphangioleiomyomatosis: New Concepts in Pathogenesis, Diagnosis, and Treatment · Riffat Meraj · 2012 · 79 citations · Cited by this paper
  36. Lymphangioleiomyomatosis: A Monogenic Model of Malignancy · Vera P. Krymskaya · 2017 · 78 citations · Cited by this paper
  37. Clinical utility of diagnostic guidelines and putative biomarkers in lymphangioleiomyomatosis · William Chang · 2012 · 72 citations · Cited by this paper
  38. TFE3-Rearranged PEComa/PEComa-like Neoplasms · Pedram Argani · 2024 · 69 citations · Cited by this paper
  39. Molecular Pathology of Lymphangioleiomyomatosis and Other Perivascular Epithelioid Cell Tumors · Guido Martignoni · 2010 · 64 citations · Cited by this paper

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